ROENTGENOLOGIC MANIFESTATIONS OF HIRSCHSPRUNG'S DISEASE IN INFANCY

¹ Director, Department of Radiology, The Children's Hospital of Philadelphia and Professor of Clinical Radiology, The School of Medicine and the Graduate School of Medicine of the University of Pennsylvania
² Associate, Department of Radiology, The Children's Hospital of Philadelphia and Associate in Radiology, the School of Medicine of the University of Pennsylvania
³ At Kimbrough Army Hospital, Fort George Meade, Maryland

During the first few months of life, Hirschsprung's disease is a potentially lethal congenital anomaly. Seldom is constipation the presenting symptom at this age. A significant number of babies presents with the picture of neonatal bowel obstruction, fulminating gastroenteritis, or chronic diarrhea with failure to thrive, the latter with protein-losing enteropathy as the extreme.

The pathognomonic roentgen signs in infancy are: (1) a zone of transition (if present); (2) irregular, bizarre contractions of aganglionic segment; (3) barium retention following a barium enema study; (4) parallel transverse folds in the dilated proximal colon; and (5) exudative enteropathy in the dilated proximal colon.

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